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jianshu322 离线
约15%的淋巴管肌瘤病患者可伴有肾脏血管平滑肌脂肪瘤.请参考下列文献中的前言部分(我有全文,如需要可提供). Angelo M. Taveira-DaSilva, Wendy K. Steagall, and Joel Moss. Lymphangioleiomyomatosis Cancer Control 2006;13:277-285. Lymphangioleiomyomatosis (LAM), a rare multisystem disorder affecting primarily women, is characterized by cystic lung lesions, lymphatic abnormalities and abdominal tumors (ie, angiomyolipomas [AMLs]).A hallmark of the disease is the proliferation of abnormal smooth muscle-like cells (LAM cells), leading to the formation of lung cysts and fluid-filled cystic structures (ie, lymphangioleiomyomas) in the axial lymphatics.AMLs, which frequently involve the kidneys, are composed of LAM cells and adipocytes, intermixed with incompletely developed vascular structures.
薄冰之旅 试译:
淋巴管平滑肌瘤病,是一种少见的、主要发生于女性的多系统障碍的疾病,主要特征是肺的囊样的病变、异常的淋巴管和腹部肿瘤的形成(如血管平滑肌脂肪瘤[AMLs])。本病的特点是异型平滑肌样细胞(LAM 细胞)的增生,引起肺囊肿和充满液体的中轴淋巴管囊性结构的形成(如 腹膜后淋巴管肌瘤)。AMLs常出现于肾脏,主要包括LAM细胞、脂肪细胞,并混未成熟的血管结构。
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